HIN-200 proteins regulate caspase activation in response to foreign cytoplasmic DNA

Science. 2009 Feb 20;323(5917):1057-60. doi: 10.1126/science.1169841. Epub 2009 Jan 8.

Abstract

The mammalian innate immune system is activated by foreign nucleic acids. Detection of double-stranded DNA (dsDNA) in the cytoplasm triggers characteristic antiviral responses and macrophage cell death. Cytoplasmic dsDNA rapidly activated caspase 3 and caspase 1 in bone marrow-derived macrophages. We identified the HIN-200 family member and candidate lupus susceptibility factor, p202, as a dsDNA binding protein that bound stably and rapidly to transfected DNA. Knockdown studies showed p202 to be an inhibitor of DNA-induced caspase activation. Conversely, the related pyrin domain-containing HIN-200 factor, AIM2 (p210), was required for caspase activation by cytoplasmic dsDNA. This work indicates that HIN-200 proteins can act as pattern recognition receptors mediating responses to cytoplasmic dsDNA.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Caspase 1 / metabolism*
  • Caspase 3 / metabolism*
  • Cell Line
  • Cytoplasm / metabolism*
  • DNA / immunology
  • DNA / metabolism*
  • DNA-Binding Proteins / isolation & purification
  • DNA-Binding Proteins / metabolism
  • Enzyme Activation
  • Immunity, Innate
  • Intracellular Signaling Peptides and Proteins / chemistry
  • Intracellular Signaling Peptides and Proteins / genetics
  • Intracellular Signaling Peptides and Proteins / isolation & purification
  • Intracellular Signaling Peptides and Proteins / metabolism*
  • Macrophages / immunology
  • Macrophages / metabolism*
  • Membrane Proteins / chemistry
  • Membrane Proteins / genetics
  • Membrane Proteins / metabolism*
  • Mice
  • Mice, Inbred Strains
  • RNA, Small Interfering
  • Receptors, Pattern Recognition / metabolism*
  • Symporters
  • Transfection

Substances

  • DNA-Binding Proteins
  • Ifi202b protein, mouse
  • Intracellular Signaling Peptides and Proteins
  • Matp protein, mouse
  • Membrane Proteins
  • RNA, Small Interfering
  • Receptors, Pattern Recognition
  • Symporters
  • DNA
  • Casp3 protein, mouse
  • Caspase 3
  • Caspase 1