Detection of CHD7 deletions by MLPA in CHARGE syndrome patients with a less typical phenotype

Eur J Med Genet. 2009 Jul-Aug;52(4):271-2. doi: 10.1016/j.ejmg.2009.02.005. Epub 2009 Feb 25.

Abstract

Bergman et al. performed a search for exon copy number alterations in the CHD7 gene using MLPA in CHARGE syndrome patients who did not have a CHD7 mutation. Based on their results they recommended to extend testing using MLPA solely in individuals with a typical CHARGE syndrome phenotype. However, since we have found deletions comprising the CHD7 gene in three patients with a less typical phenotype we recommend performing MLPA testing in all CHARGE syndrome patients without causal CHD7 mutations.

Publication types

  • Comment
  • Letter

MeSH terms

  • Coloboma / genetics*
  • DNA Helicases / genetics*
  • DNA Mutational Analysis*
  • DNA-Binding Proteins / genetics*
  • Ear / abnormalities*
  • Exons
  • Heart Defects, Congenital / genetics*
  • Humans
  • Intellectual Disability / genetics*
  • Nucleic Acid Amplification Techniques*
  • Phenotype
  • Sequence Deletion / genetics*
  • Syndrome

Substances

  • DNA-Binding Proteins
  • DNA Helicases
  • CHD7 protein, human