Detection of proteinase K resistant proteins in the urine of patients with Creutzfeldt-Jakob and other neurodegenerative diseases

Prion. 2008 Oct-Dec;2(4):170-8. doi: 10.4161/pri.2.4.8068.

Abstract

Recent concern about the possible secondary spread of vCJD through blood transfusion and blood products has highlighted the need for a sensitive test for the identification of PrP(TSE/res) in clinical specimens collected in a non-invasive way. In addition, a more accurate estimate of the prevalence of pre-clinical vCJD in the population may be possible if there were a test that could be applied to easily available material such as urine. As a step towards this goal,the detection of putative PrP(TSE/res) in the urine of CJD patients has been improved, based on Proteinase K digestion of samples and western blotting. The modified western blot uses concentrated urine as a starting material. After proteolytic treatment followed by electrophoresis and western blotting, membranes are incubated with an anti-PrP antibody conjugated directly with horseradish peroxidase. This study was conducted on urine samples of CJD and other neurodegenerative disease affected individuals. Proteinase K resistant high molecular weight proteins were detected, which are suggested to be a complex of urinary PrP and immunoglobulin proteins. Whether urine can be used as a diagnostic tool for the detection of PrP could not be answered in this study.

MeSH terms

  • Adult
  • Aged
  • Creutzfeldt-Jakob Syndrome / urine*
  • Endopeptidase K / metabolism*
  • Female
  • Humans
  • Male
  • Middle Aged
  • Neurodegenerative Diseases / urine*
  • Prions / metabolism*
  • Prions / urine*
  • Young Adult

Substances

  • Prions
  • Endopeptidase K