Key susceptibility locus for nonsyndromic cleft lip with or without cleft palate on chromosome 8q24

Nat Genet. 2009 Apr;41(4):473-7. doi: 10.1038/ng.333. Epub 2009 Mar 8.

Abstract

We conducted a genome-wide association study involving 224 cases and 383 controls of Central European origin to identify susceptibility loci for nonsyndromic cleft lip with or without cleft palate (NSCL/P). A 640-kb region at chromosome 8q24.21 was found to contain multiple markers with highly significant evidence for association with the cleft phenotype, including three markers that reached genome-wide significance. The 640-kb cleft-associated region was saturated with 146 SNP markers and then analyzed in our entire NSCL/P sample of 462 unrelated cases and 954 controls. In the entire sample, the most significant SNP (rs987525) had a P value of 3.34 x 10(-24). The odds ratio was 2.57 (95% CI = 2.02-3.26) for the heterozygous genotype and 6.05 (95% CI = 3.88-9.43) for the homozygous genotype. The calculated population attributable risk for this marker is 0.41, suggesting that this study has identified a major susceptibility locus for NSCL/P.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Chromosome Mapping
  • Chromosomes, Human, Pair 8*
  • Cleft Lip / genetics*
  • Cleft Palate / genetics
  • Family
  • Female
  • Gene Frequency
  • Genetic Carrier Screening
  • Genetic Predisposition to Disease / genetics*
  • Genotype
  • Germany
  • Homozygote
  • Humans
  • Male
  • Polymorphism, Single Nucleotide

Associated data

  • RefSeq/NM_006147
  • RefSeq/NM_031415
  • RefSeq/NM_145050
  • RefSeq/NR_003367