The treatable dementia of Sjögren's syndrome

Ann Neurol. 1991 Jul;30(1):98-101. doi: 10.1002/ana.410300117.

Abstract

Progressive dementia developed during a 15-month period in a 56-year-old woman with serologically and clinically documented primary Sjögren's syndrome. Findings from magnetic resonance imaging and angiography were normal, but a brain biopsy disclosed perivascular lymphocytic inflammation in leptomeningeal and parenchymal vessels. Treatment with high-dose corticosteroids produced rapid and nearly complete resolution of the dementia.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Alzheimer Disease / diagnosis
  • Dementia / diagnosis
  • Dementia / drug therapy
  • Dementia / etiology*
  • Diagnostic Errors
  • Female
  • Hallucinations / drug therapy
  • Hallucinations / etiology
  • Humans
  • Meningoencephalitis / drug therapy
  • Meningoencephalitis / etiology*
  • Middle Aged
  • Paranoid Behavior / drug therapy
  • Paranoid Behavior / etiology
  • Prednisone / therapeutic use*
  • Psychological Tests
  • Sjogren's Syndrome / complications*
  • Sjogren's Syndrome / drug therapy

Substances

  • Prednisone