Twenty-year survival in glioblastoma: a case report and molecular profile

Int J Radiat Oncol Biol Phys. 2009 Nov 15;75(4):1162-5. doi: 10.1016/j.ijrobp.2008.12.054. Epub 2009 Mar 26.

Abstract

Background: The prognosis for patients with glioblastoma (GB) remains grim. Historically, the median survival has been 6 to 9 months. Recent research has improved the outcome slightly. A computer search of the literature reveals few long-term survivors.

Method: Presented here is a case report of a 20-year survivor of GB, with pathologic review to confirm the diagnosis. A battery of molecular studies was performed to develop a molecular profile of this unique patient.

Results: The results of the molecular genetic testing for this most unusual patient were as follows: (1) methylguanine methyl transferase (MGMT) was methylated, (2) p53 positive, (3) PTEN tumor suppressor gene positive, (4) protein kinase AKT (pAKT) negative, and (5) epidermal growth factor receptor negative.

Conclusion: To our knowledge, this is the longest survival of any patient in the literature whose initial diagnosis was GB. Triple-positive GBM patients (MGMT methylated, PTEN, and p53 positive) are uncommon but may be associated with a better prognosis. Further research is needed to confirm whether this molecular profile is prognostic of prolonged survival. Molecular genetics will determine future treatment and prognosis in GB.

Publication types

  • Case Reports

MeSH terms

  • Antineoplastic Combined Chemotherapy Protocols / therapeutic use
  • Brain Neoplasms / chemistry*
  • Brain Neoplasms / genetics
  • Brain Neoplasms / pathology
  • Craniotomy
  • DNA Modification Methylases / analysis
  • DNA Repair Enzymes / analysis
  • ErbB Receptors / analysis
  • Fatal Outcome
  • Genes, p53
  • Glioblastoma / chemistry*
  • Glioblastoma / genetics
  • Glioblastoma / pathology
  • Humans
  • Male
  • Middle Aged
  • Neoplasm Proteins / analysis*
  • Neoplasm Proteins / genetics
  • Neoplasm Recurrence, Local / chemistry*
  • Neoplasm Recurrence, Local / pathology
  • PTEN Phosphohydrolase / analysis
  • Proto-Oncogene Proteins c-akt / analysis
  • Radiosurgery
  • Radiotherapy Dosage
  • Survivors*
  • Tumor Suppressor Proteins / analysis

Substances

  • Neoplasm Proteins
  • Tumor Suppressor Proteins
  • DNA Modification Methylases
  • MGMT protein, human
  • ErbB Receptors
  • Proto-Oncogene Proteins c-akt
  • PTEN Phosphohydrolase
  • PTEN protein, human
  • DNA Repair Enzymes