Cardiac troponins and autoimmunity: their role in the pathogenesis of myocarditis and of heart failure

Clin Immunol. 2010 Jan;134(1):80-8. doi: 10.1016/j.clim.2009.04.008. Epub 2009 May 14.

Abstract

Despite the widespread use of cardiac troponins as biomarkers for the diagnosis and quantitation of cardiac injury, the effect of troponin release and a possible autoimmune response to the troponins is unknown. Other investigators reported that programmed cell death-1 (PD-1)-receptor deficient mice developed severe cardiomyopathy with autoantibodies to troponin I. We found that immunization of genetically susceptible mice with troponin I but not troponin T induced a robust autoimmune response leading to marked inflammation and fibrosis in the myocardium. At later times, antibodies to cardiac myosin were detected in troponin-immunized mice. The severity of inflammation correlated with expression of chemokines RANTES, MIP-2, IP-10 and MCP-1 in the myocardium. Prior immunization with troponin I increased the severity of experimental infarctions, indicating that an autoimmune response to troponin I aggravates acute cardiac damage. Cardiac inflammation, fibrosis and functional impairment were transferred from immunized to naive recipients by CD4+ T cells, and the cytokine profile suggested both Th2 and Th17 profiles in A/J mice. Finally we identified an 18-mer of troponin I containing an immuno-dominant epitope.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't
  • Review

MeSH terms

  • Animals
  • Autoimmunity / immunology*
  • Cardiomyopathies / immunology
  • Cardiomyopathies / metabolism
  • Disease Models, Animal
  • Heart Failure / immunology*
  • Heart Failure / metabolism
  • Humans
  • Mice
  • Myocarditis / immunology*
  • Myocarditis / metabolism
  • Myocardium / immunology
  • Myocardium / metabolism
  • Myocardium / pathology
  • Troponin / immunology*
  • Troponin / metabolism

Substances

  • Troponin