Congenital absence of portal vein associated with nodular regenerative hyperplasia of the liver and pulmonary hypertension

Ahmet Peker; Tayfun Ucar; Zarife Kuloglu; Koray Ceyhan; Ercan Tutar; Suat Fitoz

doi:10.1016/j.clinimag.2008.12.011

Congenital absence of portal vein associated with nodular regenerative hyperplasia of the liver and pulmonary hypertension

Clin Imaging. 2009 Jul-Aug;33(4):322-5. doi: 10.1016/j.clinimag.2008.12.011.

Authors

Ahmet Peker¹, Tayfun Ucar, Zarife Kuloglu, Koray Ceyhan, Ercan Tutar, Suat Fitoz

Affiliation

¹ Department of Radiology, Ankara University, School of Medicine, Ankara, Turkey. [email protected]

PMID: 19559358
DOI: 10.1016/j.clinimag.2008.12.011

Abstract

We present a 15-year-old girl with congenital absence of the portal vein, pulmonary arterial hypertension and multiple liver lesions proven to be nodular regenerative hyperplasia with biopsy. Ultrasonography, computed tomography, and magnetic resonance imaging findings of the liver lesions and Type I portosystemic shunt are presented.

Publication types

Case Reports

MeSH terms

Adolescent
Angiography / methods*
Female
Humans
Hypertension, Pulmonary / complications*
Hypertension, Pulmonary / diagnosis*
Liver / pathology*
Portal Vein / abnormalities*
Portal Vein / diagnostic imaging*