Altered Ca2+ homeostasis in the skeletal muscle of DJ-1 null mice

Neurobiol Aging. 2011 Jan;32(1):125-32. doi: 10.1016/j.neurobiolaging.2009.07.010. Epub 2009 Aug 15.

Abstract

Loss-of-function mutations in DJ-1 are associated with early-onset of Parkinson's disease. Although DJ-1 is ubiquitously expressed, the functional pathways affected by it remain unresolved. Here we demonstrate an involvement of DJ-1 in the regulation of Ca(2+) homeostasis in mouse skeletal muscle. Using enzymatically dissociated flexor digitorum brevis muscle fibers from wild-type (wt) and DJ-1 null mice, we examined the effects of DJ-1 protein on resting, cytoplasmic [Ca(2+)] ([Ca(2+)](i)) and depolarization-evoked Ca(2+) release in the mouse skeletal muscle. The loss of DJ-1 resulted in a more than two-fold increase in resting [Ca(2+)](i). While there was no alteration in the resting membrane potential, there was a significant decrease in depolarization-evoked Ca(2+) release from the sarcoplasmic reticulum in the DJ-1 null muscle cells. Consistent with the role of DJ-1 in oxidative stress regulation and mitochondrial functional maintenance, treatments of DJ-1 null muscle cells with resveratrol, a mitochondrial activator, or glutathione, a potent antioxidant, reversed the effects of the loss of DJ-1 on Ca(2+) homeostasis. These results provide evidence of DJ-1's association with Ca(2+) regulatory pathways in mouse skeletal muscle, and suggest the potential benefit of resveratrol to functionally compensate for the loss of DJ-1.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Antioxidants / pharmacology
  • Calcium / metabolism*
  • Gene Expression Regulation / genetics
  • Homeostasis / drug effects
  • Homeostasis / genetics*
  • Membrane Potentials / drug effects
  • Membrane Potentials / genetics
  • Mice
  • Mice, Knockout
  • Muscle Cells / drug effects
  • Muscle Cells / metabolism
  • Muscle Fibers, Skeletal / drug effects
  • Muscle Fibers, Skeletal / metabolism
  • Muscle, Skeletal / cytology
  • Muscle, Skeletal / metabolism*
  • Muscle, Skeletal / physiology
  • Oncogene Proteins / deficiency*
  • Peroxiredoxins
  • Protein Deglycase DJ-1
  • Resveratrol
  • Ryanodine Receptor Calcium Release Channel / metabolism
  • Sarcoplasmic Reticulum Calcium-Transporting ATPases / metabolism
  • Stilbenes / pharmacology

Substances

  • Antioxidants
  • Atp2a1 protein, mouse
  • Oncogene Proteins
  • Ryanodine Receptor Calcium Release Channel
  • Stilbenes
  • Peroxiredoxins
  • PARK7 protein, mouse
  • Protein Deglycase DJ-1
  • Sarcoplasmic Reticulum Calcium-Transporting ATPases
  • Resveratrol
  • Calcium