Antithrombin III-Amiens: a new family with an Arg47----Cys inherited variant of antithrombin III with impaired heparin cofactor activity

Am J Hematol. 1991 Jan;36(1):25-9. doi: 10.1002/ajh.2830360106.

Abstract

A family with an antithrombin III variant (AT-III-Amiens) demonstrating abnormal heparin cofactor activity is described. Amplification and direct sequencing of genomic DNA by the polymerase chain reaction procedure permitted the identification of an Arg47----Cys mutation in exon 2 of the variant antithrombin III gene.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Alleles
  • Antithrombin III / chemistry
  • Antithrombin III / genetics*
  • Antithrombin III / metabolism*
  • Base Sequence
  • Blood Coagulation Tests
  • DNA / analysis
  • Female
  • Genetic Variation*
  • Humans
  • Molecular Sequence Data
  • Mutation
  • Polymerase Chain Reaction

Substances

  • Antithrombin III
  • DNA