Right ventricular hypertrabeculation associated with double-outlet left ventricle: exaggeration of a normal pattern or right ventricular cardiomyopathy?

J Cardiovasc Med (Hagerstown). 2010 Mar;11(3):193-5. doi: 10.2459/JCM.0b013e32833134e9.

Abstract

We describe a rare case of double-outlet left ventricle, ventricular septal defect, and subpulmonary valve stenosis surgically corrected by Rastelli procedure, developing severe homograft obstruction with right ventricular dilation and extensive hypertrabeculation/noncompaction during follow-up. We briefly discuss the cause diagnosis, and clinical significance of right ventricular hypertrabeculation/noncompaction.

Publication types

  • Case Reports

MeSH terms

  • Abnormalities, Multiple*
  • Adolescent
  • Blood Vessel Prosthesis Implantation / adverse effects*
  • Cardiac Catheterization
  • Cardiomyopathies / diagnosis*
  • Cardiomyopathies / etiology
  • Dilatation, Pathologic
  • Double Outlet Right Ventricle / complications
  • Double Outlet Right Ventricle / surgery*
  • Echocardiography, Doppler, Color
  • Heart Valve Prosthesis Implantation / adverse effects*
  • Heart Ventricles / pathology
  • Humans
  • Isolated Noncompaction of the Ventricular Myocardium / complications
  • Isolated Noncompaction of the Ventricular Myocardium / diagnosis*
  • Magnetic Resonance Imaging
  • Male
  • Pulmonary Valve Stenosis / complications
  • Pulmonary Valve Stenosis / surgery*