Association of JAG1 with bone mineral density and osteoporotic fractures: a genome-wide association study and follow-up replication studies

Am J Hum Genet. 2010 Feb 12;86(2):229-39. doi: 10.1016/j.ajhg.2009.12.014. Epub 2010 Jan 21.

Abstract

Bone mineral density (BMD), a diagnostic parameter for osteoporosis and a clinical predictor of fracture, is a polygenic trait with high heritability. To identify genetic variants that influence BMD in different ethnic groups, we performed a genome-wide association study (GWAS) on 800 unrelated Southern Chinese women with extreme BMD and carried out follow-up replication studies in six independent study populations of European descent and Asian populations including 18,098 subjects. In the meta-analysis, rs2273061 of the Jagged1 (JAG1) gene was associated with high BMD (p = 5.27 x 10(-8) for lumbar spine [LS] and p = 4.15 x 10(-5) for femoral neck [FN], n = 18,898). This SNP was further found to be associated with the low risk of osteoporotic fracture (p = 0.009, OR = 0.7, 95% CI 0.57-0.93, n = 1881). Region-wide and haplotype analysis showed that the strongest association evidence was from the linkage disequilibrium block 5, which included rs2273061 of the JAG1 gene (p = 8.52 x 10(-9) for LS and 3.47 x 10(-5) at FN). To assess the function of identified variants, an electrophoretic mobility shift assay demonstrated the binding of c-Myc to the "G" but not "A" allele of rs2273061. A mRNA expression study in both human bone-derived cells and peripheral blood mononuclear cells confirmed association of the high BMD-related allele G of rs2273061 with higher JAG1 expression. Our results identify the JAG1 gene as a candidate for BMD regulation in different ethnic groups, and it is a potential key factor for fracture pathogenesis.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Aged
  • Alleles
  • Bone Density / genetics*
  • Calcium-Binding Proteins / genetics*
  • Cohort Studies
  • Electrophoretic Mobility Shift Assay
  • Female
  • Follow-Up Studies
  • Fractures, Bone / complications*
  • Fractures, Bone / genetics
  • Fractures, Bone / physiopathology
  • Gene Expression Regulation
  • Genetic Predisposition to Disease*
  • Genome-Wide Association Study*
  • Humans
  • Intercellular Signaling Peptides and Proteins / genetics*
  • Jagged-1 Protein
  • Membrane Proteins / genetics*
  • Middle Aged
  • Osteoporosis / complications*
  • Osteoporosis / genetics*
  • Osteoporosis / physiopathology
  • Polymorphism, Single Nucleotide / genetics
  • Reproducibility of Results
  • Serrate-Jagged Proteins

Substances

  • Calcium-Binding Proteins
  • Intercellular Signaling Peptides and Proteins
  • JAG1 protein, human
  • Jagged-1 Protein
  • Membrane Proteins
  • Serrate-Jagged Proteins