Congenital mitral disease: anomalous mitral arcade in a young man

Ann Thorac Surg. 2010 Feb;89(2):629-31. doi: 10.1016/j.athoracsur.2009.07.070.

Abstract

We present the case of a 33-year-old man referred to our institution with a diagnosis of severe mitral valvular stenosis and insufficiency. We realized the valvular disease was due to an "anomalous mitral arcade," a rare congenital malformation of the mitral tensor apparatus characterized by enlarged papillary muscles connected to mitral leaflets by a typical fibrous tissue bridge. This arrangement creates a fibrous continuity between valvular and subvalvular apparatus. The reported echocardiographic images shows in detail the anatomic and functional features of this rare condition.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Biocompatible Materials
  • Chordae Tendineae / abnormalities*
  • Chordae Tendineae / diagnostic imaging
  • Chordae Tendineae / surgery*
  • Diagnosis, Differential
  • Echocardiography*
  • Heart Defects, Congenital / diagnostic imaging*
  • Heart Defects, Congenital / surgery*
  • Humans
  • Male
  • Mitral Valve / abnormalities*
  • Mitral Valve / diagnostic imaging
  • Mitral Valve / surgery*
  • Mitral Valve Insufficiency / congenital*
  • Mitral Valve Insufficiency / diagnostic imaging
  • Mitral Valve Insufficiency / surgery*
  • Mitral Valve Stenosis / congenital*
  • Mitral Valve Stenosis / diagnostic imaging
  • Mitral Valve Stenosis / surgery*
  • Papillary Muscles / abnormalities*
  • Papillary Muscles / diagnostic imaging
  • Papillary Muscles / surgery*
  • Polytetrafluoroethylene
  • Postoperative Complications / diagnostic imaging

Substances

  • Biocompatible Materials
  • Polytetrafluoroethylene