Mesoportal bypass for extrahepatic portal vein obstruction in children: close to a cure for most!

J Pediatr Surg. 2010 Jan;45(1):272-6. doi: 10.1016/j.jpedsurg.2009.08.019.

Abstract

Aim: Extrahepatic portal vein obstruction (EPVO) is a common cause of portal hypertension in children and can lead to life-threatening bleeding, thrombocytopenia, and coagulation disorders. Mesoportal bypass (MPB) restores normal physiologic portal flow to the liver and corrects portal hypertension. There is, however, little long-term outcome data after MPB. The aim of our study was to analyze the long-term outcome after MPB in children.

Methods: Retrospective single-center review of all MPB with more than 5-year follow-up was performed in children between 1998 and 2003.

Results: Thirty children underwent MPB, which was successful in 29. Long-term follow-up is available for 24. Median age at the time of bypass was 8.5 years (range, 0.4-14.2 years). Material used for bypass was as follows: left internal jugular vein (n = 20), recanalized umbilical vein (n = 2), gastric vein, and a large colic vein (n = 2). Median time since MPB is 8 years (range, 5.3-8.8 years). One MPB using recanalized umbilical vein thrombosed at 4 months but was successfully refashioned using Gortex. One MPB with left internal jugular vein was thrombosed at 1 year after cardiac surgery. Overall, 23 of 24 children have a patent bypass and resolution of portal hypertension. All showed an decrease in spleen size. Recurrent blood flow in the cavernoma with secondary increase in spleen size occurred in 5 children (median time, 3.4 years after MPB). Further evaluation of these 5 revealed no recurrence of portal hypertension.

Conclusion: The MPB provides long-term correction of portal hypertension owing to EPVO. Where technically feasible, MPB is the preferred surgical procedure for treatment of EPVO.

Publication types

  • Comparative Study

MeSH terms

  • Adolescent
  • Child
  • Child, Preschool
  • Female
  • Follow-Up Studies
  • Humans
  • Hypertension, Portal / etiology
  • Hypertension, Portal / surgery*
  • Infant
  • Jugular Veins / surgery
  • Jugular Veins / transplantation
  • Liver Circulation / physiology
  • Longitudinal Studies
  • Male
  • Mesenteric Veins / surgery*
  • Portal Vein / surgery*
  • Portasystemic Shunt, Surgical / methods*
  • Postoperative Complications / surgery
  • Recurrence
  • Thrombosis / surgery
  • Transplantation, Autologous
  • Treatment Outcome
  • Umbilical Veins / surgery
  • Umbilical Veins / transplantation
  • Vascular Patency / physiology
  • Venous Thrombosis / complications
  • Venous Thrombosis / surgery*