Acute posterior multifocal placoid pigment epitheliopathy with cerebral involvement

J Neurol Neurosurg Psychiatry. 1991 Jan;54(1):77-9. doi: 10.1136/jnnp.54.1.77.

Abstract

In a patient with angiographically proven cerebral vasculitis five months after acute posterior multifocal placoid pigment epitheliopathy (APMPPE) neurological symptoms promptly responded to steroid treatment. Cerebrospinal fluid (CSF) showed a lymphocytic pleocytosis. Magnetic resonance imaging (MRI) revealed multifocal white matter lesions in the hemispheres and the brain stem suggesting a diffuse subcortical vasculitis.

Publication types

  • Case Reports

MeSH terms

  • Cerebral Arterial Diseases / diagnosis*
  • Cerebral Arterial Diseases / drug therapy
  • Cerebral Arterial Diseases / pathology
  • Dexamethasone / administration & dosage
  • Drug Therapy, Combination
  • Fluorescein Angiography
  • Humans
  • Magnetic Resonance Imaging
  • Male
  • Methylprednisolone / administration & dosage
  • Middle Aged
  • Pigment Epithelium of Eye / pathology*
  • Vasculitis / diagnosis*
  • Vasculitis / drug therapy
  • Vasculitis / pathology

Substances

  • Dexamethasone
  • Methylprednisolone