Peritoneal pseudomyxoma arising from the urachus

Alejandra Martínez; Gwénael Ferron; Eliane Mery; Laurance Gladieff; Jean Pierre Delord; Denis Querleu

doi:10.1016/j.suronc.2009.12.004

Peritoneal pseudomyxoma arising from the urachus

Surg Oncol. 2012 Mar;21(1):1-5. doi: 10.1016/j.suronc.2009.12.004. Epub 2010 Feb 26.

Authors

Alejandra Martínez¹, Gwénael Ferron, Eliane Mery, Laurance Gladieff, Jean Pierre Delord, Denis Querleu

Affiliation

¹ Institut Claudius Regaud, Surgery, 20-24, Rue du Pont Saint Pierre, 31052 Toulouse, France. [email protected]

PMID: 20189378
DOI: 10.1016/j.suronc.2009.12.004

Abstract

Pseudomyxoma peritonei (PMP) arising from urachal tumors is extremely rare. To our knowledge, natural history, tumor biological behaviour, morbidity, treatment, and prognosis of PMP arising from the urachus are determined by the associated PMP. Management of urachal tumors with associated PMP should be based on aggressive locorregional therapy with cytoreductive surgery and hyperthermic intraperitoneal chemotherapy, similar to PMP arising from other origins.

Publication types

Case Reports
Research Support, Non-U.S. Gov't
Review

MeSH terms

Adenocarcinoma / diagnosis
Adenocarcinoma / drug therapy
Adenocarcinoma / surgery*
Adult
Cystadenocarcinoma, Mucinous / diagnosis
Cystadenocarcinoma, Mucinous / drug therapy
Cystadenocarcinoma, Mucinous / surgery*
Humans
Magnetic Resonance Imaging
Male
Peritoneal Neoplasms / diagnosis
Peritoneal Neoplasms / drug therapy
Peritoneal Neoplasms / surgery*
Pseudomyxoma Peritonei / diagnosis
Pseudomyxoma Peritonei / drug therapy
Pseudomyxoma Peritonei / surgery*
Rare Diseases / diagnosis
Rare Diseases / drug therapy
Rare Diseases / surgery*
Retreatment
Tomography, X-Ray Computed
Urinary Bladder Neoplasms / diagnosis
Urinary Bladder Neoplasms / drug therapy
Urinary Bladder Neoplasms / surgery*

Supplementary concepts

Urachal adenocarcinoma