Progress in epidermolysis bullosa research: toward treatment and cure

J Invest Dermatol. 2010 Jul;130(7):1778-84. doi: 10.1038/jid.2010.90. Epub 2010 Apr 15.

Abstract

Epidermolysis bullosa (EB) is a clinically and genetically heterogeneous group of blistering disorders with considerable morbidity and mortality. Two decades ago, EB entered the molecular era with the identification of mutations in specific genes expressed within the cutaneous basement membrane zone; mutations in 14 genes have now been identified. This progress has now formed the basis for development of novel molecular therapies for this disease.

Publication types

  • Review

MeSH terms

  • Biomedical Research / trends*
  • Dermatology / trends*
  • Epidermolysis Bullosa / physiopathology*
  • Epidermolysis Bullosa / therapy*
  • Humans