Annular lichenoid dermatosis of youth is a recently described skin disease with particular clinicopathological features. It has been so far described in 35 patients, all of whom (but one) were white. We report here the first case of annular lichenoid dermatosis of youth in a Japanese patient, who is the youngest reported with this diagnosis, and briefly review the salient clinicopathological features of this condition. Our observation shows that annular lichenoid dermatosis of youth can also affect Japanese patients; therefore, Japanese dermatologists should be aware of this particular dermatosis.