Immunohematologic reconstitution in pediatric patients after T cell-depleted HLA-haploidentical stem cell transplantation for thalassemia

Biol Blood Marrow Transplant. 2010 Nov;16(11):1557-66. doi: 10.1016/j.bbmt.2010.05.003. Epub 2010 Jun 25.

Abstract

To analyze immunohematologic reconstitution, particularly of natural killer (NK) cells, we evaluated 13 β-thalassemia patients after 20 and 60 days and 1 year posttransplantation with T cell-depleted HLA-haploidentical stem cells. We assessed lymphocyte and bone marrow (BM) progenitor cell phenotype and differentiation capacity, spontaneous BM cytokine production, stromal cells, and stromal cell interleukin (IL)-7 production. A reduced clonogenic capability manifested at day +20. Patients had significantly lower CD4(+) T cells versus controls, mainly in the CD45RA(+)CD62L(+) subset. NKs were among the first lymphocytes to repopulate the peripheral blood. At day +60, an increase in primitive BM progenitor cells paralleled small increases in CD4(+), naïve CD4(+), and thymic naïve Th cells. A significant increase in CD4(+) and CD8(+) markers paralleled an increase in CD3⁻CD16(+) NKs, especially with full engraftment. In patients with stable mixed chimerism we observed very low levels of CD3(+) donor chimerism early after transplant that increased over time, but a stable population of high donor NK cells, suggesting a role of these cells on donor engraftment. Stromal cells secreted less IL-7 and displayed "macrophage-like" morphology. Patients initially manifested impaired stem/progenitor cell growth and differentiation capacity in parallel with altered T cell homeostasis and a reduced T cell naïve compartment. We hypothesize that T cell compartment damage partly arises from altered new T cell production from the hematopoietic stem/progenitor cells under stromal cytokine influence. NNK subset analysis might be useful for determining transplant outcome.

Publication types

  • Clinical Trial
  • Research Support, Non-U.S. Gov't

MeSH terms

  • B-Lymphocytes / cytology
  • Blood Cells / cytology
  • Bone Marrow Cells / cytology
  • Bone Marrow Cells / metabolism
  • CD4-Positive T-Lymphocytes / cytology
  • CD8-Positive T-Lymphocytes / cytology
  • Cell Count
  • Child
  • Child, Preschool
  • Chimera / blood
  • Colony-Forming Units Assay
  • Graft Rejection / immunology
  • Graft Survival / immunology
  • HLA Antigens / genetics
  • HLA Antigens / immunology
  • Hematopoietic Stem Cell Transplantation / methods*
  • Histocompatibility, Maternal-Fetal*
  • Humans
  • Interleukin-2 / metabolism
  • Interleukin-7 / metabolism
  • Killer Cells, Natural / cytology
  • Living Donors
  • Lymphocyte Count
  • Lymphocyte Depletion*
  • Lymphocytes / cytology*
  • Mothers
  • Stromal Cells / cytology
  • Stromal Cells / metabolism
  • T-Lymphocyte Subsets / cytology
  • T-Lymphocytes / cytology*
  • Transplants
  • Treatment Outcome
  • Tumor Necrosis Factor-alpha / metabolism
  • beta-Thalassemia / therapy*

Substances

  • HLA Antigens
  • IL7 protein, human
  • Interleukin-2
  • Interleukin-7
  • Tumor Necrosis Factor-alpha