Complement factor h autoantibodies and age-related macular degeneration

Invest Ophthalmol Vis Sci. 2010 Nov;51(11):5858-63. doi: 10.1167/iovs.09-5124. Epub 2010 Jun 30.

Abstract

Purpose: In this case-control study, the hypothesis that factor H autoantibodies are associated with age-related macular degeneration (AMD) was examined.

Methods: One hundred AMD patients (median age, 78 years), 98 age-matched control subjects (median age, 78 years) known not to have AMD, and 100 healthy blood donors (median age, 43 years) were enrolled. An enzyme-linked immunosorbent assay (ELISA) was used to screen for complement factor H autoantibodies and either quantitative polymerase chain reaction (qPCR) or multiplex ligation-dependent probe amplification (MLPA) were performed to measure the copy number of the gene encoding complement factor H-related protein 3 (CFHR3).

Results: There was a significant difference in the median complement factor H autoantibody titer between the three groups (AMD patients, 196 reference units [RU]]; age-match control subjects, 316 RU; and blood donor control subjects, 121 RU; Kruskal-Wallis test, P < 0.001). Pair-wise comparison (Mann-Whitney test) showed that all three groups were significantly different from each other. Two different thresholds were used in the healthy blood donors to identify individuals with complement factor H autoantibodies. Both suggested that the prevalence of factor H autoantibodies was decreased in AMD patients. The CFHR3 copy number was measured as a surrogate for the deletion of the genes encoding complement factor H-related proteins 3 and 1 (CFHR3/1). The allele frequency of the deletion was significantly higher in the age-matched control subjects than in the AMD patients (22.2% vs. 8.2%).

Conclusions: The level of factor H autoantibodies is lower in AMD patients than in age-matched control subjects.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Adult
  • Aged
  • Aged, 80 and over
  • Autoantibodies / blood*
  • Blood Donors
  • Blood Proteins / genetics
  • Case-Control Studies
  • Complement C3b Inactivator Proteins / genetics
  • Complement Factor H / immunology
  • DNA Primers / chemistry
  • DNA Probes / chemistry
  • Enzyme-Linked Immunosorbent Assay
  • Female
  • Gene Dosage
  • Gene Frequency
  • Humans
  • Macular Degeneration / immunology*
  • Male
  • Middle Aged
  • Nucleic Acid Amplification Techniques
  • Polymerase Chain Reaction
  • Young Adult

Substances

  • Autoantibodies
  • Blood Proteins
  • CFH protein, human
  • CFHR1 protein, human
  • CFHR3 protein, human
  • Complement C3b Inactivator Proteins
  • DNA Primers
  • DNA Probes
  • Complement Factor H