Bullous lupus: an unusual initial presentation of systemic lupus erythematosus in an adolescent girl

Pediatr Dermatol. 2010 Jul-Aug;27(4):373-6. doi: 10.1111/j.1525-1470.2010.01179.x.

Abstract

Bullous systemic lupus erythematosus is a subepidermal blistering disease that occurs only rarely in a subset of patients with systemic lupus erythematosus and even less commonly in pediatric patients. Autoimmunity in bullous systemic lupus erythematosus is characterized by the presence of circulating anti-type VII collagen antibodies. We report here a case of a child whose initial systemic lupus erythematosus presentation was a diffuse bullous eruption.

MeSH terms

  • Adolescent
  • Anti-Inflammatory Agents / therapeutic use
  • Antibodies, Antinuclear / blood
  • Autoantibodies / blood
  • Collagen Type VII / immunology
  • Dapsone / therapeutic use
  • Female
  • Humans
  • Hydroxychloroquine / therapeutic use
  • Lupus Erythematosus, Cutaneous / diagnosis*
  • Lupus Erythematosus, Cutaneous / drug therapy
  • Lupus Erythematosus, Cutaneous / immunology
  • Lupus Erythematosus, Cutaneous / pathology
  • Lupus Erythematosus, Systemic / diagnosis*
  • Lupus Erythematosus, Systemic / drug therapy
  • Lupus Erythematosus, Systemic / immunology
  • Lupus Erythematosus, Systemic / pathology
  • Methylprednisolone / therapeutic use
  • Mycophenolic Acid / analogs & derivatives
  • Mycophenolic Acid / therapeutic use
  • Prednisone / therapeutic use
  • Skin Diseases, Vesiculobullous / diagnosis*
  • Skin Diseases, Vesiculobullous / drug therapy
  • Skin Diseases, Vesiculobullous / immunology
  • Skin Diseases, Vesiculobullous / pathology

Substances

  • Anti-Inflammatory Agents
  • Antibodies, Antinuclear
  • Autoantibodies
  • Collagen Type VII
  • Hydroxychloroquine
  • Dapsone
  • Mycophenolic Acid
  • Prednisone
  • Methylprednisolone