Protective effects of transduced PEP-1-Frataxin protein on oxidative stress-induced neuronal cell death

J Neurol Sci. 2010 Nov 15;298(1-2):64-9. doi: 10.1016/j.jns.2010.08.016.

Abstract

Reactive oxygen species (ROS) actively contribute to the development of a number of human diseases including ischemia. In response to oxidative stress, frataxin has a significant ability to improve cell survival though its biological function is unclear in relation to ischemia. To explore frataxin's role in protecting against ischemic cell death, we constructed PEP-1-Frataxin cell-permeable fusion protein. In a dose- and time-dependent manner PEP-1-Frataxin rapidly transduced into astrocyte cells and protected them against oxidative stress-induced cell death. Further, using an animal model, immunohistochemical analysis revealed that PEP-1-Frataxin prevented neuronal cell death in the CA1 region of the hippocampus induced by transient forebrain ischemia. These results demonstrate that transduced PEP-1-Frataxin protects against cell death in vitro and in vivo, suggesting that transduction of PEP-1-Frataxin could be useful as a therapeutic agent for various human diseases related to oxidative stress.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Astrocytes / drug effects
  • Blood-Brain Barrier / metabolism
  • CA1 Region, Hippocampal / pathology
  • Cell Death / drug effects
  • Cell Line, Tumor
  • Coloring Agents
  • Cysteamine / analogs & derivatives*
  • Cysteamine / pharmacology
  • Dose-Response Relationship, Drug
  • Frataxin
  • Genetic Vectors
  • Gerbillinae
  • Humans
  • Iron-Binding Proteins / biosynthesis
  • Iron-Binding Proteins / pharmacology*
  • Ischemic Attack, Transient / drug therapy
  • Ischemic Attack, Transient / pathology
  • Microscopy, Fluorescence
  • Neurons / drug effects*
  • Neuroprotective Agents*
  • Oxidative Stress / drug effects*
  • Peptides / pharmacology*
  • Rats
  • Recombinant Fusion Proteins / biosynthesis
  • Recombinant Fusion Proteins / pharmacology
  • Tetrazolium Salts
  • Thiazoles
  • Transduction, Genetic

Substances

  • Coloring Agents
  • Iron-Binding Proteins
  • Neuroprotective Agents
  • Pep-1 peptide
  • Peptides
  • Recombinant Fusion Proteins
  • Tetrazolium Salts
  • Thiazoles
  • Cysteamine
  • thiazolyl blue