Helmet-delivered heliox-CPAP in severe upper airway obstruction caused by PHACES syndrome

A Vivanco-Allende; J Mayordomo-Colunga; A Coca-Pelaz; C Rey; A Medina

doi:10.1002/ppul.21367

Helmet-delivered heliox-CPAP in severe upper airway obstruction caused by PHACES syndrome

Pediatr Pulmonol. 2011 Mar;46(3):306-8. doi: 10.1002/ppul.21367. Epub 2010 Oct 21.

Authors

A Vivanco-Allende¹, J Mayordomo-Colunga, A Coca-Pelaz, C Rey, A Medina

Affiliation

¹ Pediatric Intensive Care Unit, Hospital Universitario Central de Asturias, Ovideo, Asturias, Spain. [email protected].

PMID: 20967839
DOI: 10.1002/ppul.21367

Abstract

We present the case of a 4-month-old girl with PHACES syndrome and severe upper respiratory airway obstruction secondary to multiple subglottic and tracheal hemangiomas effectively treated with heliox-CPAP delivered by helmet (HH-CPAP).

Keywords: PHACES syndrome; airway obstruction; heliox; helmet; non-invasive ventilation.

Publication types

Case Reports

MeSH terms

Airway Obstruction / etiology*
Airway Obstruction / therapy*
Aortic Coarctation / complications*
Continuous Positive Airway Pressure / instrumentation*
Eye Abnormalities / complications*
Female
Helium / administration & dosage*
Humans
Infant
Neurocutaneous Syndromes / complications*
Oxygen / administration & dosage*
Severity of Illness Index
Syndrome

Substances

Helium
heliox
Oxygen

Supplementary concepts

PHACE association