Mitogen accumulation in von Recklinghausen neurofibromatosis

Ann Neurol. 1990 Mar;27(3):298-303. doi: 10.1002/ana.410270312.

Abstract

Most, but not all, patients with von Recklinghausen neurofibromatosis develop tumors (neurofibromas) that contain large numbers of Schwann cells and fibroblasts. To begin to understand the molecular events that contribute to cell proliferation in these benign tumors, we have analyzed extracts of neurofibromas to determine whether they contain mitogens for Schwann cells or fibroblasts, or both. Schwann cell and fibroblast mitogens are present in neurofibroma extracts. All the neurofibromas analyzed contain a Schwann cell mitogen similar to a neuronal cell surface molecule known to stimulate Schwann cell proliferation during normal development; this mitogen also stimulates fibroblast proliferation. Basic fibroblast growth factor is present in 60% of tumors evaluated. Accumulation of mitogenic substances may contribute to the growth of neurofibromas.

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Cell Division / drug effects
  • Fibroblasts / cytology*
  • Fibroblasts / drug effects
  • Growth Substances / isolation & purification
  • Growth Substances / metabolism*
  • Humans
  • Neurofibromatosis 1 / metabolism*
  • Peripheral Nervous System Neoplasms / metabolism*
  • Schwann Cells / cytology*
  • Schwann Cells / drug effects
  • Skin Neoplasms / metabolism*

Substances

  • Growth Substances