Primary hypertrophic osteoarthropathy

Rheumatol Int. 2012 Mar;32(3):607-10. doi: 10.1007/s00296-010-1667-z. Epub 2010 Dec 2.

Abstract

Pachydermoperiostosis PDP (idiopathic or primary hypertrophic osteoarthropathy) is a rare congenital disease that inherited in an autosomal fashion. The disease is more common in males and develops gradually from adulthood. The disease is characterized by coarse facial features, clubbing of the fingers and radiographic periostitis of the distal long bones. The patient was a 37-year-old man with acroosteolysis and digital clubbing of hands and feet fingers and lion facies.

Publication types

  • Case Reports

MeSH terms

  • Acromegaly / diagnosis
  • Adult
  • Diagnosis, Differential
  • Facies
  • Humans
  • Male
  • Osteitis / complications
  • Osteitis / pathology
  • Osteoarthropathy, Primary Hypertrophic / complications
  • Osteoarthropathy, Primary Hypertrophic / diagnosis*
  • Osteoarthropathy, Primary Hypertrophic / diagnostic imaging
  • Osteoarthropathy, Secondary Hypertrophic / complications
  • Osteoarthropathy, Secondary Hypertrophic / diagnosis
  • Osteoarthropathy, Secondary Hypertrophic / pathology
  • Osteolysis / complications
  • Osteolysis / pathology
  • Radiography
  • Syphilis / complications
  • Syphilis / diagnosis