Epigenetic regulation of PAX5 expression in acute T-cell lymphoblastic leukemia

Leuk Res. 2011 May;35(5):614-9. doi: 10.1016/j.leukres.2010.11.015. Epub 2010 Dec 14.

Abstract

The analysis of genomic alterations in acute lymphoblastic leukemia (ALL) has provided new insights for prognosis and possible targets of novel therapies. In T-ALL the role of molecular abnormalities has still to be determined. Deregulated promoter hypermethylation of critical genes like PAX5 may have a significant impact on the course of ALL. Samples derived from 75 patients with ALL (B-ALL = 24, T-ALL = 51) and from healthy volunteers were analyzed. PAX5 expression was assessed by micro-array analysis (HG-U133plus 2.0) and correlated with promoter CpG island methylation of PAX5 using a pyrosequencing approach. The analyzed CpG marks in the promoter region of PAX5 were completely and uniformly unmethylated in the control group of healthy individuals. The T-ALL cases featured even higher methylation levels (median: 20%) with a strong variation of values of up to 85% methylation. Analysis of the association of altered methylation levels with gene expression data indicated a differential epigenetic regulation of PAX5 through promoter methylation which may contribute to the pathogenesis of this disease.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Aged
  • Aged, 80 and over
  • Base Sequence
  • Case-Control Studies
  • CpG Islands / genetics
  • DNA Methylation
  • Epigenesis, Genetic / physiology*
  • Female
  • Gene Expression Regulation, Leukemic*
  • Humans
  • Male
  • Middle Aged
  • Molecular Sequence Data
  • PAX5 Transcription Factor / genetics*
  • Precursor T-Cell Lymphoblastic Leukemia-Lymphoma / genetics*
  • Promoter Regions, Genetic / genetics
  • Young Adult

Substances

  • PAX5 Transcription Factor
  • PAX5 protein, human