Nephrotic syndrome after allogeneic hematopoietic stem cell transplantation: etiology and pathogenesis

Blood Cells Mol Dis. 2011 Feb 15;46(2):182-7. doi: 10.1016/j.bcmd.2010.12.003. Epub 2011 Jan 5.

Abstract

In this study we investigated the etiology and pathogenesis of nephrotic syndrome (NS) after allogeneic hematopoietic stem cell transplantation (allo-HSCT) in 257 patients with hematopoietic malignancies who survived more than 2 months post allo-HSCT. Associations of NS with the conditioning regimen, graft versus host disease (GVHD), and other variables were analyzed. Pathologic features of the kidney, regulatory T cells (Tregs), interferon-γ (IFN-γ), and tumor necrosis factor-α (TNF-α) were studied. NS was identified in 9 patients. The number of Tregs at day+30, 60, 90, and 180 was lower in NS patients than non-NS patients (P=0.001, 0.001, 0.007, 0.003). Serum levels of IFN-γ and TNF-α were higher in NS patients (P=0.032, 0.001, respectively). NS post allo-HSCT was associated with the occurrence of chronic GVHD (P=0.02). NS post-HSCT is an immune disorder that may involve immune complex deposition, Th1 cytokines, and Tregs.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Antigens, CD
  • Biopsy
  • Female
  • Graft vs Host Disease / blood
  • Graft vs Host Disease / etiology*
  • Graft vs Host Disease / immunology
  • Graft vs Host Disease / pathology
  • Hematologic Neoplasms / therapy
  • Hematopoietic Stem Cell Transplantation / adverse effects*
  • Humans
  • Immunohistochemistry
  • Interferon-gamma / blood
  • Male
  • Nephrotic Syndrome / etiology*
  • Nephrotic Syndrome / pathology
  • T-Lymphocytes, Regulatory / immunology
  • Transplantation, Homologous / adverse effects*
  • Tumor Necrosis Factor-alpha / blood

Substances

  • Antigens, CD
  • Tumor Necrosis Factor-alpha
  • Interferon-gamma