Functional total anomalous pulmonary venous drainage by left atrium-to-superior vena cava shunt

Ann Thorac Surg. 2011 Mar;91(3):903-4. doi: 10.1016/j.athoracsur.2010.08.039.

Abstract

Total anomalous pulmonary venous connection is occasionally associated with a functional single ventricle and is thought to be a risk for the staged Fontan approach. We report a patient with a very rare presentation of mitral atresia and intact atrial septum with physiologically total anomalous pulmonary venous drainage by a connecting vein between the left atrium and the superior vena cava. A surgical atrioseptectomy as a functional repair of total anomalous pulmonary venous connection and pulmonary artery banding was successfully performed as the first palliation for Fontan completion.

Publication types

  • Case Reports

MeSH terms

  • Anastomosis, Surgical
  • Cardiac Surgical Procedures / methods*
  • Child, Preschool
  • Female
  • Heart Atria / abnormalities*
  • Heart Atria / surgery
  • Heart Defects, Congenital / surgery*
  • Humans
  • Pulmonary Veins / abnormalities*
  • Pulmonary Veins / surgery
  • Vena Cava, Superior / abnormalities*
  • Vena Cava, Superior / surgery