Hypoplastic left heart syndrome with restrictive atrial septum and advanced heart block documented with a novel fetal electrocardiographic monitor

Ultrasound Obstet Gynecol. 2011 Oct;38(4):472-4. doi: 10.1002/uog.8982. Epub 2011 Sep 6.

Abstract

Hypoplastic left ventricle with congenital heart block has been reported previously in a fetus with concurrent left atrial isomerism and levo-transposition of the great arteries. We present the unusual case of an infant diagnosed in utero with hypoplastic left heart syndrome, a restrictive atrial septum and advanced heart block but with D-looping of the ventricles and no atrial isomerism. In addition, fetal heart rhythm was documented with the assistance of a new fetal electrocardiographic monitor.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Atrial Septum / embryology
  • Atrial Septum / physiopathology*
  • Electrocardiography / instrumentation*
  • Fatal Outcome
  • Female
  • Heart Block / congenital*
  • Heart Block / diagnosis
  • Heart Block / embryology
  • Heart Block / surgery
  • Heart Septal Defects, Atrial / diagnosis*
  • Heart Septal Defects, Atrial / embryology
  • Heart Septal Defects, Atrial / surgery
  • Humans
  • Hypoplastic Left Heart Syndrome / diagnosis*
  • Hypoplastic Left Heart Syndrome / embryology
  • Hypoplastic Left Heart Syndrome / physiopathology
  • Hypoplastic Left Heart Syndrome / surgery
  • Pregnancy

Supplementary concepts

  • Congenital heart block