Selective elimination of pathogenic synovial fluid T-cells from rheumatoid arthritis and juvenile idiopathic arthritis by targeted activation of Fas-apoptotic signaling

Immunol Lett. 2011 Aug 30;138(2):161-8. doi: 10.1016/j.imlet.2011.04.004. Epub 2011 Apr 15.

Abstract

In Rheumatoid Arthritis (RA) and Juvenile Idiopathic Arthritis (JIA) elimination of autoreactive T-cells by FasL/Fas-mediated Activation-Induced Cell Death (AICD) appears to be inhibited resulting in the perpetuation of the inflammatory response and concomitant progressive tissue destruction. Here, we report on a novel strategy that aims to overcome the local inhibition of AICD by using rationally designed recombinant fusion proteins in which sFasL is genetically fused to a T-cell selective targeting domain. The series included sFasL fusion proteins with engineered binding specificity for various T-cell surface-expressed proteins including CD7, CD28, RANKL and CD40L. The proposed mode of action is that selective binding of a given sFasL fusion protein results in its accretion at the cell surface of T-cells only, displaying a surplus of sFasL that is available to reactivate AICD in pathogenic synovial T-cells. Of the series of T-cell targeting FasL fusion proteins a CD7-targeted fusion protein, designated scFvCD7:sFasL, proved to be the most potent, with significant pro-apoptotic activity towards synovial fluid T-cells in all patient samples tested (RA; n=22: JIA; n=6). Treatment with scFvCD7:sFasL induced up to 80% apoptosis in CD3-positive synovial T-cells. Importantly, scFvCD7:sFasL potently activated Fas-signaling in synovial T(H1)-cells as well as synovial T(reg) cells, but not in synovial T(H2) cells. These findings indicate that scFvCD7:sFasL may be of therapeutic value for the selective elimination of pathogenic synovial T-cells of the T(H1) subtype in both RA and JIA.

MeSH terms

  • Adolescent
  • Adult
  • Aged
  • Aged, 80 and over
  • Antigens, CD7 / immunology*
  • Antigens, CD7 / metabolism
  • Apoptosis* / drug effects
  • Apoptosis* / immunology
  • Arthritis, Juvenile* / drug therapy
  • Arthritis, Juvenile* / immunology
  • Arthritis, Juvenile* / metabolism
  • Arthritis, Juvenile* / pathology
  • CD3 Complex / immunology*
  • Child
  • Child, Preschool
  • Fas Ligand Protein / chemistry
  • Fas Ligand Protein / immunology
  • Fas Ligand Protein / metabolism
  • Fas Ligand Protein / pharmacology*
  • Female
  • Humans
  • Lymphocyte Activation
  • Lymphocyte Depletion*
  • Male
  • Middle Aged
  • RANK Ligand / immunology
  • RANK Ligand / metabolism
  • Recombinant Fusion Proteins / chemistry
  • Recombinant Fusion Proteins / immunology
  • Recombinant Fusion Proteins / metabolism
  • Recombinant Fusion Proteins / pharmacology*
  • Signal Transduction / drug effects
  • Synovial Fluid / cytology
  • Synovial Fluid / drug effects
  • Synovial Fluid / immunology*
  • Synovial Fluid / metabolism
  • T-Lymphocytes* / drug effects
  • T-Lymphocytes* / immunology
  • Th1-Th2 Balance / drug effects
  • fas Receptor / immunology
  • fas Receptor / metabolism

Substances

  • Antigens, CD7
  • CD3 Complex
  • Fas Ligand Protein
  • RANK Ligand
  • Recombinant Fusion Proteins
  • TNFSF11 protein, human
  • fas Receptor