Thrombotic thrombocytopenic purpura in IgG4-related disease with severe deficiency of ADAMTS-13 activity and IgG4 autoantibody against ADAMTS-13

Arthritis Care Res (Hoboken). 2011 Aug;63(8):1209-12. doi: 10.1002/acr.20484.
No abstract available

Publication types

  • Case Reports

MeSH terms

  • ADAM Proteins / deficiency*
  • ADAM Proteins / immunology
  • ADAMTS13 Protein
  • Autoantibodies / blood*
  • Autoantibodies / immunology
  • Autoimmune Diseases / blood
  • Autoimmune Diseases / complications*
  • Autoimmune Diseases / diagnosis
  • Autoimmune Diseases / immunology
  • Humans
  • Immunoglobulin G / blood*
  • Immunoglobulin G / immunology
  • Male
  • Middle Aged
  • Purpura, Thrombotic Thrombocytopenic / blood
  • Purpura, Thrombotic Thrombocytopenic / complications*
  • Purpura, Thrombotic Thrombocytopenic / pathology
  • Purpura, Thrombotic Thrombocytopenic / therapy
  • Severity of Illness Index
  • Treatment Outcome

Substances

  • Autoantibodies
  • Immunoglobulin G
  • ADAM Proteins
  • ADAMTS13 Protein
  • ADAMTS13 protein, human