Eyes wide shut--unusual two stage repair of pectus excavatum and annuloaortic ectasia in a 37 year old marfan patient: case report

J Cardiothorac Surg. 2011 May 2:6:64. doi: 10.1186/1749-8090-6-64.

Abstract

We report about a 37 year old male patient with a pectus excavatum. The patient was in NYHA functional class III. After performed computed tomography the symptoms were thought to be related to the severity of chest deformation. A Ravitch-procedure had been accomplished in a district hospital in 2009. The crack of a metal bar led to a reevaluation 2010, in which surprisingly the presence of an annuloaortic ectasia (root 73×74 mm) in direct neighborhood of the formerly implanted metal-bars was diagnosed. Echocardiography revealed a severe aortic valve regurgitation, the left ventricle was massively dilated presenting a reduced ejection fraction of 45%. A marfan syndrome was suspected and the patient underwent a valve sparing aortic root replacement (David procedure) in our institution with an uneventful postoperative course. A review of the literature in combination with discussion of our case suggests the application of stronger recommendations towards preoperative cardiovascular assessment in patients with pectus excavatum.

Publication types

  • Case Reports

MeSH terms

  • Abnormalities, Multiple*
  • Adult
  • Aortic Aneurysm, Thoracic / congenital
  • Aortic Aneurysm, Thoracic / diagnosis
  • Aortic Aneurysm, Thoracic / surgery*
  • Aortic Diseases / congenital
  • Aortic Diseases / diagnosis
  • Aortic Diseases / surgery*
  • Echocardiography, Transesophageal
  • Electrocardiography
  • Follow-Up Studies
  • Funnel Chest / diagnosis
  • Funnel Chest / surgery*
  • Humans
  • Male
  • Marfan Syndrome / diagnosis
  • Marfan Syndrome / surgery*
  • Orthopedic Procedures / methods*
  • Tomography, X-Ray Computed
  • Vascular Surgical Procedures / methods*