Clinical profile of hearing loss in children with congenital cytomegalovirus (CMV) infection: CMV DNA diagnosis using preserved umbilical cord

Acta Otolaryngol. 2011 Sep;131(9):976-82. doi: 10.3109/00016489.2011.583268. Epub 2011 May 26.

Abstract

Conclusions: Congenital cytomegalovirus (CMV) infection is a major cause of bilateral and unilateral sensorineural hearing loss (SNHL) in children, accounting for 9.0% of SNHL cases. The diagnostic rate using combined genetic deafness test and CMV DNA detection test was determined to be 46.4% in bilateral profound SNHL.

Objectives: The present study investigated the prevalence of congenital CMV infection diagnosed retrospectively by detection of CMV DNA in dried umbilical cord specimens from children with unilateral or bilateral SNHL up to the age of 12 years.

Methods: Preserved dried umbilical cords were collected from 134 children with bilateral (46 children) or unilateral (88 children) SNHL. DNA was extracted from the dried umbilical cords and CMV DNA was detected by quantitative PCR. Genetic deafness tests based on the invader assay were performed in children with bilateral SNHL.

Results: CMV DNA from the dried umbilical cords was detected in 8.7% of the bilateral SNHL and 9.1% of unilateral SNHL. Deafness gene mutations were identified in 21.7% (10/46) of children with bilateral SNHL.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Audiometry, Pure-Tone
  • Child
  • Child, Preschool
  • Connexin 26
  • Connexins / genetics
  • Cytomegalovirus / genetics*
  • Cytomegalovirus / isolation & purification
  • Cytomegalovirus Infections / congenital*
  • Cytomegalovirus Infections / diagnosis*
  • Cytomegalovirus Infections / virology*
  • DNA Mutational Analysis
  • DNA, Viral / genetics*
  • Deafness / congenital*
  • Deafness / diagnosis*
  • Deafness / virology*
  • Female
  • Humans
  • Infant
  • Male
  • Membrane Transport Proteins / genetics
  • Real-Time Polymerase Chain Reaction
  • Retrospective Studies
  • Sulfate Transporters
  • Tissue Preservation
  • Umbilical Cord / virology*

Substances

  • Connexins
  • DNA, Viral
  • Membrane Transport Proteins
  • SLC26A4 protein, human
  • Sulfate Transporters
  • Connexin 26