Sclerodermatous chronic graft-versus-host disease induced by host T-cell-mediated autoimmunity

Immunol Cell Biol. 2012 Mar;90(3):358-67. doi: 10.1038/icb.2011.46. Epub 2011 May 31.

Abstract

Despite a long-standing hypothesis that chronic graft-versus-host disease (cGVHD) is an autoimmune disorder, most mouse models of cGVHD have been developed on the assumption that donor T cells are essential for its development. Here we show that cGVHD may be caused by autoreactive host T cells in mice that have been lethally irradiated and grafted with T-cell-depleted allogeneic bone marrow cells. In this chimera, host T cells derived from radioresistant intrathymic T-cell precursors caused dermal fibrosis and periportal inflammation, without the requirement for donor T cells. The lack of host DCs within the thymus after high-dose irradiation allowed autoreactive host T cells to escape thymic negative selection. Moreover, the homeostatic expansion of these T cells may augment their autoreactivity. These findings indicate that host T-cell-mediated cGVHD is an autoimmune process that occurs following the grafting of T-cell-depleted BM cells into hosts with functioning thymuses. We propose, based on the present data, that host T-cell-dependent autoimmunity is a potential mechanism by which cGVHD is induced.

MeSH terms

  • Animals
  • Autoimmunity
  • Bone Marrow Transplantation*
  • Cells, Cultured
  • Chronic Disease
  • Clonal Selection, Antigen-Mediated
  • Dendritic Cells / immunology*
  • Graft vs Host Disease / complications
  • Graft vs Host Disease / immunology*
  • Immune Tolerance
  • Mice
  • Mice, Inbred Strains
  • Mice, Knockout
  • Mice, Transgenic
  • Scleroderma, Limited / etiology
  • Scleroderma, Limited / immunology*
  • T-Lymphocyte Subsets / immunology
  • T-Lymphocyte Subsets / metabolism*
  • T-Lymphocyte Subsets / pathology
  • T-Lymphocytes, Regulatory / immunology
  • T-Lymphocytes, Regulatory / metabolism*
  • T-Lymphocytes, Regulatory / pathology
  • Thymus Gland / immunology
  • Thymus Gland / pathology
  • Transplantation Chimera