Aplasia cutis congenita: impact of early treatment on calvarial osteogenesis

J Plast Reconstr Aesthet Surg. 2011 Sep;64(9):e237-40. doi: 10.1016/j.bjps.2010.11.011. Epub 2011 Jul 7.

Abstract

We describe an infant with severe aplasia cutis congenita of the scalp that was characterised by a full-thickness calvarial bone defect combined with the absence of dura mater complicated by sagittal sinus haemorrhage. The defect was successfully managed by closure with a local temporal flap combined with a periosteum patch to allow closure of the dura mater. Previously, conservative treatments failed to remedy unexpected, massive bleeding, which could potentially threaten a patient's life. We highlight the osteogenic potential of surgically manipulated dura mater in this patient who was managed early with a surgical approach.

Publication types

  • Case Reports

MeSH terms

  • Dura Mater / abnormalities
  • Ectodermal Dysplasia / surgery*
  • Hemorrhage / etiology
  • Hemorrhage / surgery
  • Humans
  • Infant
  • Male
  • Osteogenesis*
  • Periosteum / transplantation*
  • Skull / abnormalities
  • Skull / growth & development*
  • Skull / surgery*
  • Superior Sagittal Sinus
  • Surgical Flaps*