The microcephaly-capillary malformation syndrome

Am J Med Genet A. 2011 Sep;155A(9):2080-7. doi: 10.1002/ajmg.a.34118. Epub 2011 Aug 3.

Abstract

We report on three children from two families with a new pattern recognition malformation syndrome consisting of severe congenital microcephaly (MIC), intractable epilepsy including infantile spasms, and generalized capillary malformations that was first reported recently in this journal [Carter et al. (2011); Am J Med Genet A 155: 301-306]. Two of our reported patients are an affected brother and sister, suggesting this is an autosomal recessive severe congenital MIC syndrome.

Publication types

  • Case Reports

MeSH terms

  • Abnormalities, Multiple / genetics*
  • Adolescent
  • Capillaries / abnormalities*
  • Dermis / blood supply*
  • Epilepsy
  • Female
  • Humans
  • Infant
  • Infant, Newborn
  • Male
  • Microcephaly / genetics*
  • Septo-Optic Dysplasia
  • Young Adult

Supplementary concepts

  • Optic nerve hypoplasia, familial bilateral