c-kit gene mutation and CD117 expression in human anorectal melanomas

Hum Pathol. 2012 Jun;43(6):801-7. doi: 10.1016/j.humpath.2011.08.005. Epub 2011 Dec 9.

Abstract

c-kit and BRAF mutations play an important role during the pathogenesis of melanoma. The subtypes of melanomas arising from different parts of the body have variable c-kit or BRAF mutation frequencies. Few studies in the literature have examined c-kit and BRAF mutation status in melanomas that occur in the anus and rectum. In this study, we analyzed 40 cases of anorectal melanoma for c-kit and BRAF mutations by DNA sequencing using paraffin-embedded tissues. c-kit Mutations were detected in exons 9, 11, 13, and 17. CD117 expression in tumor cells was analyzed by immunohistochemistry. Our study showed that a c-kit mutation was found in 7 of the 40 cases of anorectal melanoma. CD117 expression was detected in 16 of the 40 cases, and 3 of these 16 cases also had c-kit mutations. Mutations in BRAF were also identified in 2 patients. These results indicate that a subset of anorectal melanomas have activating c-kit mutations, which suggests that kinase inhibitors such as imatinib may be used to treat this subset of melanoma patients. In addition, our results show that c-kit mutations do not correlate with CD117 expression.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Aged
  • Anus Neoplasms / genetics*
  • Anus Neoplasms / metabolism
  • Base Sequence
  • Biomarkers, Tumor / analysis
  • DNA Mutational Analysis
  • Female
  • Humans
  • Immunohistochemistry
  • Male
  • Melanoma / genetics*
  • Melanoma / metabolism
  • Middle Aged
  • Molecular Sequence Data
  • Mutation*
  • Proto-Oncogene Proteins c-kit / biosynthesis*
  • Proto-Oncogene Proteins c-kit / genetics*
  • Real-Time Polymerase Chain Reaction
  • Rectal Neoplasms / genetics*
  • Rectal Neoplasms / metabolism

Substances

  • Biomarkers, Tumor
  • Proto-Oncogene Proteins c-kit