IgM nephropathy in India: a single centre experience

Indian J Pediatr. 2012 Aug;79(8):1025-7. doi: 10.1007/s12098-012-0693-0.

Abstract

Objective: To find out the incidence and natural history of IgMN in India.

Methods: Renal biopsies of children ≤12 y age of last 6 y were retrospectively evaluated. Their clinical and biochemical presentation were correlated. Patients with systemic diseases/disorders were excluded from the study.

Results: Immunoglobulin M nephropathy (IgMN) constituted 11.9% (n = 28) of 236 renal biopsies. Mean age was 10 y, predominant in boys (n = 24), most of the patients presented with proteinuria and edema. The most common associated histopathological finding was mesangial proliferative glomerulonephritis (MePGN) in 60.7% (n = 17) followed by minimal change disease (MCD) in 28.6% (n = 8) and focal segmental glomerulosclerosis (FSGS) in 10.7% (n = 3). In 85.7%, IgM appeared as the sole immunoglobulin deposit mainly in mesangial regions, followed by accompanied C3 in 3.6% (n = 1) and C1q + C3 in 10.7% (n = 3) biopsies.

Conclusions: IgMN was observed in 11.9% biopsies with commonest morphology of MePGN followed by MCD and FSGS; proteinuria was bad prognosticator in addition to FSGS and co-deposition of other immunoglobulins had no significance.

MeSH terms

  • Biomarkers / metabolism
  • Biopsy
  • Child
  • Child, Preschool
  • Female
  • Glomerulonephritis / complications
  • Glomerulonephritis / epidemiology
  • Glomerulonephritis / immunology*
  • Glomerulonephritis / pathology
  • Glomerulonephritis, Membranoproliferative / complications
  • Glomerulonephritis, Membranoproliferative / epidemiology
  • Glomerulonephritis, Membranoproliferative / immunology
  • Glomerulonephritis, Membranoproliferative / pathology
  • Glomerulosclerosis, Focal Segmental / complications
  • Glomerulosclerosis, Focal Segmental / epidemiology
  • Glomerulosclerosis, Focal Segmental / immunology
  • Glomerulosclerosis, Focal Segmental / pathology
  • Humans
  • Immunoglobulin M / metabolism*
  • Incidence
  • India / epidemiology
  • Infant
  • Kidney / immunology*
  • Kidney / pathology
  • Male
  • Nephrosis, Lipoid / complications
  • Nephrosis, Lipoid / epidemiology
  • Nephrosis, Lipoid / immunology
  • Nephrosis, Lipoid / pathology
  • Nephrotic Syndrome / complications
  • Nephrotic Syndrome / epidemiology
  • Nephrotic Syndrome / immunology*
  • Nephrotic Syndrome / pathology
  • Retrospective Studies

Substances

  • Biomarkers
  • Immunoglobulin M