Blood basophils from cystic fibrosis patients with allergic bronchopulmonary aspergillosis are primed and hyper-responsive to stimulation by aspergillus allergens

J Cyst Fibros. 2012 Dec;11(6):502-10. doi: 10.1016/j.jcf.2012.04.008. Epub 2012 May 16.

Abstract

Introduction: Fifteen to sixty percent of cystic fibrosis patients harbor Aspergillus fumigatus (Af) in their airways (CF-AC) and some will develop allergic bronchopulmonary aspergillosis (CF-ABPA). Since basophils play a key role in allergy, we hypothesized that they would display alterations in CF-ABPA patients compared to CF-AC or patients without Af colonization (CF).

Methods: Using flow cytometry, we measured CD203c, CD63 and CD123 levels on basophils from CF-ABPA (N=11), CF-AC (N=14), and CF (N=12) patients before and after ex vivo stimulation with Af allergens.

Results: Baseline CD203c was increased in basophils from CF-ABPA compared to CF-AC and CF patients. Af extract and recombinant Aspf1 stimulated basophils from CF-ABPA patients to markedly upregulate CD203c, along with modest upregulation of CD63 and a CD123 downward trend. Plasma TARC/CCL17 at baseline and post-stimulation cell supernatant histamine levels were similar in the three groups.

Conclusions: In CF-ABPA, blood basophils are primed and hyperresponsive to Af allergen stimulation.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Adult
  • Allergens / immunology
  • Allergens / pharmacology
  • Antigens, Fungal / immunology
  • Aspergillosis, Allergic Bronchopulmonary / immunology*
  • Aspergillus fumigatus / immunology*
  • Basophils / cytology
  • Basophils / immunology*
  • Basophils / metabolism
  • Cell Degranulation / immunology
  • Chemokine CCL17 / blood
  • Child
  • Cystic Fibrosis / immunology*
  • Cystic Fibrosis / microbiology
  • Female
  • Flow Cytometry
  • Fungal Proteins / immunology
  • Fungal Proteins / pharmacology
  • Humans
  • Interleukin-3 Receptor alpha Subunit / metabolism
  • Male
  • Phosphoric Diester Hydrolases / metabolism
  • Pyrophosphatases / metabolism
  • Recombinant Proteins / immunology
  • Tetraspanin 30 / metabolism
  • Young Adult

Substances

  • ASPF1 protein, Aspergillus fumigatus
  • Allergens
  • Antigens, Fungal
  • CCL17 protein, human
  • CD63 protein, human
  • Chemokine CCL17
  • ENPP3 protein, human
  • Fungal Proteins
  • IL3RA protein, human
  • Interleukin-3 Receptor alpha Subunit
  • Recombinant Proteins
  • Tetraspanin 30
  • Phosphoric Diester Hydrolases
  • Pyrophosphatases