Immunopathogenesis of Graves' ophthalmopathy: the role of the TSH receptor

Best Pract Res Clin Endocrinol Metab. 2012 Jun;26(3):281-9. doi: 10.1016/j.beem.2011.10.003.

Abstract

Graves' ophthalmopathy is an inflammatory autoimmune disorder of the orbit. The close clinical and temporal relationships between Graves' hyperthyroidism and ophthalmopathy have long suggested that both conditions derive from a single systemic process and share the thyrotropin receptor as a common autoantigen. This receptor is expressed not only in thyroid follicular cells, but also in orbital fibroblasts with higher levels measured in orbital cells from ophthalmopathy patients than in cells from normal individuals. Recent studies from several laboratories have shown that thyrotropin receptor activation in orbital fibroblasts enhances hyaluronic acid synthesis and adipogenesis, both cellular functions that appear to be upregulated in the diseased orbit. The phosphoinositide 3-kinase/Akt signaling cascade, along with other effector pathways including adenylyl cyclase/cAMP, appears to mediate these processes. Future therapies for this condition may involve inhibition of thyrotropin receptor signaling in orbital fibroblasts.

Publication types

  • Research Support, N.I.H., Extramural
  • Review

MeSH terms

  • Animals
  • Anti-Inflammatory Agents, Non-Steroidal / pharmacology
  • Anti-Inflammatory Agents, Non-Steroidal / therapeutic use
  • Graves Ophthalmopathy / drug therapy
  • Graves Ophthalmopathy / immunology*
  • Graves Ophthalmopathy / metabolism
  • Graves Ophthalmopathy / pathology
  • Humans
  • Immunoglobulins, Thyroid-Stimulating / analysis*
  • Ligands
  • Molecular Targeted Therapy
  • Orbit / drug effects
  • Orbit / immunology
  • Orbit / metabolism
  • Orbit / pathology
  • Receptor, IGF Type 1 / chemistry
  • Receptor, IGF Type 1 / metabolism
  • Receptors, Thyrotropin / agonists
  • Receptors, Thyrotropin / antagonists & inhibitors
  • Receptors, Thyrotropin / chemistry
  • Receptors, Thyrotropin / metabolism
  • Signal Transduction / drug effects

Substances

  • Anti-Inflammatory Agents, Non-Steroidal
  • Immunoglobulins, Thyroid-Stimulating
  • Ligands
  • Receptors, Thyrotropin
  • thyrotropin-binding inhibitory immunoglobulin
  • Receptor, IGF Type 1