DEF6, a novel substrate for the Tec kinase ITK, contains a glutamine-rich aggregation-prone region and forms cytoplasmic granules that co-localize with P-bodies

J Biol Chem. 2012 Sep 7;287(37):31073-84. doi: 10.1074/jbc.M112.346767. Epub 2012 Jul 24.

Abstract

Localization of DEF6 (SLAT/IBP), a Rho-family guanine nucleotide exchange factor, to the center of the immune synapse is dependent upon ITK, a Tec-family kinase that regulates the spatiotemporal organization of components of T cell signaling pathways and Cdc42-dependent actin polymerization. Here we demonstrate that ITK both interacts with DEF6 and phosphorylates DEF6 at tyrosine residues Tyr(210) and Tyr(222). Expression of a GFP-tagged Y210E-Y222E phosphomimic resulted in the formation of DEF6 cytoplasmic granules that co-localized with decapping enzyme 1 (DCP1), a marker of P-bodies; sites of mRNA degradation. Similarly treatment of cells with puromycin or sodium arsenite, reagents that arrest translation, also resulted in the accumulation of DEF6 in cytoplasmic granules. Bioinformatics analysis identified a glutamine-rich, heptad-repeat region; a feature of aggregating proteins, within the C-terminal region of DEF6 with the potential to promote granule formation through a phosphorylation-dependent unmasking of this region. These data suggest that in addition to its role as a GEF, DEF6 may also function in regulating mRNA translation.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Arsenates / pharmacology
  • COS Cells
  • Chlorocebus aethiops
  • Cytoplasmic Granules / genetics
  • Cytoplasmic Granules / metabolism*
  • DNA-Binding Proteins / genetics
  • DNA-Binding Proteins / metabolism*
  • Endoribonucleases / genetics
  • Endoribonucleases / metabolism
  • Guanine Nucleotide Exchange Factors / genetics
  • Guanine Nucleotide Exchange Factors / metabolism*
  • Humans
  • Jurkat Cells
  • Nuclear Proteins / genetics
  • Nuclear Proteins / metabolism*
  • Phosphorylation / drug effects
  • Phosphorylation / physiology
  • Protein Biosynthesis / drug effects
  • Protein Biosynthesis / physiology
  • Protein Structure, Tertiary
  • Protein Synthesis Inhibitors / pharmacology
  • Protein-Tyrosine Kinases / genetics
  • Protein-Tyrosine Kinases / metabolism*
  • Puromycin / pharmacology
  • RNA Stability / drug effects
  • RNA Stability / physiology
  • RNA, Messenger / genetics
  • RNA, Messenger / metabolism

Substances

  • Arsenates
  • DEF6 protein, human
  • DNA-Binding Proteins
  • Guanine Nucleotide Exchange Factors
  • Nuclear Proteins
  • Protein Synthesis Inhibitors
  • RNA, Messenger
  • Puromycin
  • sodium arsenate
  • Protein-Tyrosine Kinases
  • emt protein-tyrosine kinase
  • Endoribonucleases
  • DCP1b protein, human