Pituitary stalk Langerhans cell histiocytosis treated with CyberKnife radiosurgery

Clin Neurol Neurosurg. 2013 May;115(5):573-7. doi: 10.1016/j.clineuro.2012.07.004. Epub 2012 Jul 25.

Abstract

Objective: Langerhans cell histiocytosis (LCH) is a rare idiopathic disease that is characterized by clonal proliferation of Langerhans histiocytes in various parts of the body. These atypical cells have been found to infiltrate single or multiple organs, including bone, lungs, liver, spleen, lymph nodes, and skin. Central nervous system invasion in LCH patients has rarely been reported, especially in the adult population.

Methods and results: We describe three histopathologically confirmed cases of adult LCH that involves both the pituitary stalk and hypothalamus, and report our limited experience of such cases in this location that has been treated with CyberKnife radio surgery.

Conclusion: The treatment goal of controlling lesion growth is achieved by CyberKnife radiosurgery in this case series. All patients tolerated the treatment well without obvious complications.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Biopsy
  • Brain / pathology
  • Diabetes Insipidus / complications
  • Diabetes, Gestational / pathology
  • Female
  • Histiocytosis, Langerhans-Cell / pathology
  • Histiocytosis, Langerhans-Cell / surgery*
  • Hormone Replacement Therapy
  • Humans
  • Hypothalamus / pathology
  • Magnetic Resonance Imaging
  • Male
  • Middle Aged
  • Optic Chiasm / pathology
  • Pituitary Diseases / pathology
  • Pituitary Diseases / surgery*
  • Pituitary Gland / pathology
  • Pituitary Gland / surgery*
  • Pituitary Hormones / therapeutic use
  • Polyuria / etiology
  • Pregnancy
  • Radiosurgery / methods*
  • Thirst
  • Visual Fields / physiology

Substances

  • Pituitary Hormones