The endovascular management of a neurofibromatosis vasculopathy: a case report

Vasc Endovascular Surg. 2012 Oct;46(7):575-7. doi: 10.1177/1538574412454583. Epub 2012 Jul 31.

Abstract

We describe the management of a 30-year-old male with type I neurofibromatosis who required an above-knee amputation for bleeding, infection, swelling, and multiple severe joint instability. Postoperatively, he continued to bleed from the stump site. Angiography revealed multiple small distal bleeding aneurysms. Hemostasis was eventually achieved with standard microcoil embolization.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Amputation Stumps / blood supply
  • Amputation Stumps / diagnostic imaging
  • Amputation Stumps / surgery*
  • Amputation, Surgical / adverse effects*
  • Debridement
  • Embolization, Therapeutic
  • Endovascular Procedures*
  • Humans
  • Male
  • Negative-Pressure Wound Therapy
  • Neurofibromatosis 1 / complications
  • Neurofibromatosis 1 / diagnosis
  • Neurofibromatosis 1 / surgery
  • Neurofibromatosis 1 / therapy*
  • Postoperative Hemorrhage / diagnostic imaging
  • Postoperative Hemorrhage / etiology
  • Postoperative Hemorrhage / therapy*
  • Radiography
  • Reoperation
  • Sepsis / etiology
  • Sepsis / surgery
  • Treatment Outcome
  • Vascular Diseases / diagnostic imaging
  • Vascular Diseases / etiology
  • Vascular Diseases / surgery*