An unexpected cause of respiratory distress and cyanosis: cardiac inflammatory myofibroblastic tumor

Congenit Heart Dis. 2013 Nov-Dec;8(6):E174-7. doi: 10.1111/chd.12026. Epub 2012 Dec 27.

Abstract

Inflammatory myofibroblastic tumor is an uncommon spindle cell tumor, occurring mainly in children and young adults. It is an extremely rare cardiac tumor especially patients under 1 year. Although it is benign, the tumor may be very aggressive locally. The diagnosis of this unusual pediatric cardiac tumor without pathologic specimens is difficult. We report a rare case of inflammatory myofibroblastic tumors of the right ventricle in a 7-month-old girl presenting with respiratory distress and cyanosis.

Keywords: Cyanosis; Infant; Inflammatory Myofibroblastic Tumor; Respiratory Distress.

Publication types

  • Case Reports

MeSH terms

  • Cardiac Surgical Procedures
  • Cyanosis / diagnosis
  • Cyanosis / etiology*
  • Echocardiography, Doppler, Color
  • Fatal Outcome
  • Female
  • Heart Neoplasms / complications*
  • Heart Neoplasms / diagnosis
  • Heart Neoplasms / surgery
  • Humans
  • Infant
  • Lung Diseases / diagnosis
  • Lung Diseases / etiology*
  • Neoplasms, Muscle Tissue / complications*
  • Neoplasms, Muscle Tissue / diagnosis
  • Neoplasms, Muscle Tissue / surgery
  • Treatment Outcome