Antigen recognition by autoreactive CD4⁺ thymocytes drives homeostasis of the thymic medulla

PLoS One. 2012;7(12):e52591. doi: 10.1371/journal.pone.0052591. Epub 2012 Dec 27.

Abstract

The thymic medulla is dedicated for purging the T-cell receptor (TCR) repertoire of self-reactive specificities. Medullary thymic epithelial cells (mTECs) play a pivotal role in this process because they express numerous peripheral tissue-restricted self-antigens. Although it is well known that medulla formation depends on the development of single-positive (SP) thymocytes, the mechanisms underlying this requirement are incompletely understood. We demonstrate here that conventional SP CD4⁺ thymocytes bearing autoreactive TCRs drive a homeostatic process that fine-tunes medullary plasticity in adult mice by governing the expansion and patterning of the medulla. This process exhibits strict dependence on TCR-reactivity with self-antigens expressed by mTECs, as well as engagement of the CD28-CD80/CD86 costimulatory axis. These interactions induce the expression of lymphotoxin α in autoreactive CD4⁺ thymocytes and RANK in mTECs. Lymphotoxin in turn drives mTEC development in synergy with RANKL and CD40L. Our results show that Ag-dependent interactions between autoreactive CD4⁺ thymocytes and mTECs fine-tune homeostasis of the medulla by completing the signaling axes implicated in mTEC expansion and medullary organization.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Autoantigens / immunology*
  • Body Patterning
  • CD4 Antigens / metabolism*
  • CD40 Antigens / metabolism
  • CD40 Ligand / metabolism
  • Cell Proliferation
  • Epithelial Cells / metabolism
  • Epithelial Cells / physiology
  • Female
  • Gene Expression
  • Homeostasis*
  • Lymphotoxin beta Receptor / metabolism
  • Lymphotoxin-alpha / genetics
  • Lymphotoxin-alpha / metabolism
  • Male
  • Mice
  • Mice, Inbred C57BL
  • Mice, Knockout
  • Receptor Activator of Nuclear Factor-kappa B / metabolism
  • Signal Transduction
  • Thymocytes / immunology
  • Thymocytes / metabolism
  • Thymocytes / physiology*
  • Thymus Gland / cytology
  • Thymus Gland / growth & development*
  • Thymus Gland / immunology
  • Tissue Culture Techniques

Substances

  • Autoantigens
  • CD4 Antigens
  • CD40 Antigens
  • Lymphotoxin beta Receptor
  • Lymphotoxin-alpha
  • Receptor Activator of Nuclear Factor-kappa B
  • Tnfrsf11a protein, mouse
  • CD40 Ligand

Grants and funding

MI was supported by grants from the Swiss National Science Foundation (PZ00P3-131945, http://www.snf.ch) and the Jules Thorn foundation (http://www.julesthorntrust.org.uk). Work in the laboratory of WR was supported by the Swiss National Science Foundation (grant 31003A-127255, http://www.snf.ch). LG was supported by fellowships from the Association de la Recherche sur le Cancer (http://www.arc-cancer.net) and the ANR (http://www.agence-nationale-recherche.fr). The laboratory of OL was funded by the Ligue Contre le Cancer (http://www.liguecancer.ch/fr), Inserm (http://www.inserm.fr) and Institut Curie (curie.fr). The funders had no role in study design, data collection and analysis, decision to publish, or preparation of the manuscript.