Inclusions in frontotemporal lobar degeneration with TDP-43 proteinopathy (FTLD-TDP) and amyotrophic lateral sclerosis (ALS), but not FTLD with FUS proteinopathy (FTLD-FUS), have properties of amyloid

Acta Neuropathol. 2013 Mar;125(3):463-5. doi: 10.1007/s00401-013-1089-6. Epub 2013 Feb 3.
No abstract available

Publication types

  • Letter

MeSH terms

  • Amyloid / metabolism*
  • Amyotrophic Lateral Sclerosis / pathology*
  • Basophils / pathology
  • Basophils / ultrastructure
  • DNA-Binding Proteins / metabolism*
  • Frontotemporal Lobar Degeneration / pathology*
  • Humans
  • Inclusion Bodies / pathology
  • Inclusion Bodies / ultrastructure
  • Motor Cortex / metabolism*
  • Motor Cortex / pathology
  • Motor Cortex / ultrastructure
  • RNA-Binding Protein FUS / metabolism

Substances

  • Amyloid
  • DNA-Binding Proteins
  • RNA-Binding Protein FUS