Abstract
Dominant-negative TGF-β receptor II (dnTGF-βRII) mice spontaneously develop an autoimmune cholangitis resembling human primary biliary cirrhosis (PBC). Interestingly, the dominant-negative TGF-β receptor is expressed by both CD4(+) and CD8(+) T cells and leads to greatly reduced (but not absent) TGF-β signaling resulting in T cell intrinsic cell mediated autoimmunity. However, the mechanisms of the T cell dysregulation remain unclear. Recently it has been shown that TGF-β signaling is intimately involved with miRNA biogenesis and control. Herein we show that lack of T cell TGF-β signaling leads to down regulation of T cell miRNAs but up-regulation of the key inflammatory miRNA 21. Furthermore, the expression of miR-21 from hepatic effector CD8(+) T cells is significantly higher than in the same subsets isolated from spleen and mesenteric lymph nodes of the dnTGF-βRII mice. Previous studies indicate that miR-21 increases the synthesis of IFN-γ and IL-17A by T cells and suppresses apoptosis via programmed cell death protein 4 (PDCD4). Data presented herein demonstrate that transfecting w.t. B6 T cell subsets with miR-21 resulted in up-regulation of the inflammatory cytokines TNF-α and IFN-γ, thus partly replicating the dnTGF-βRII T cell phenotype. In conclusion, these data suggest miR-21 plays a critical role in the production of pro-inflammatory cytokines in dnTGF-βRII mice, which could be a contributing factor for the development of the organ-specific autoimmune cholangitis and colitis in this murine model of human PBC.
Copyright © 2013 Elsevier Ltd. All rights reserved.
Publication types
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Research Support, N.I.H., Extramural
MeSH terms
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Animals
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Apoptosis Regulatory Proteins / immunology
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Apoptosis Regulatory Proteins / metabolism
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Autoimmune Diseases / genetics
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Autoimmune Diseases / immunology
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Autoimmune Diseases / metabolism
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CD4-Positive T-Lymphocytes / immunology
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CD4-Positive T-Lymphocytes / metabolism
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CD8-Positive T-Lymphocytes / immunology
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CD8-Positive T-Lymphocytes / metabolism
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Cholangitis / genetics
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Cholangitis / immunology
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Cholangitis / metabolism
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Cytokines / immunology*
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Cytokines / metabolism
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Flow Cytometry
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Gene Expression / immunology
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Humans
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Inflammation Mediators / immunology*
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Inflammation Mediators / metabolism
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Interferon-gamma / immunology
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Interferon-gamma / metabolism
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Interleukin-17 / immunology
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Interleukin-17 / metabolism
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Liver / immunology
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Liver / metabolism
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Liver / pathology
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Liver Cirrhosis, Biliary / genetics
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Liver Cirrhosis, Biliary / immunology
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Liver Cirrhosis, Biliary / metabolism
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Mice
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Mice, Inbred C57BL
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Mice, Transgenic
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MicroRNAs / genetics
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MicroRNAs / immunology*
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Protein Serine-Threonine Kinases / genetics
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Protein Serine-Threonine Kinases / immunology*
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Protein Serine-Threonine Kinases / metabolism
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RNA-Binding Proteins / immunology
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RNA-Binding Proteins / metabolism
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Receptor, Transforming Growth Factor-beta Type II
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Receptors, Transforming Growth Factor beta / genetics
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Receptors, Transforming Growth Factor beta / immunology*
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Receptors, Transforming Growth Factor beta / metabolism
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Reverse Transcriptase Polymerase Chain Reaction
Substances
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Apoptosis Regulatory Proteins
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Cytokines
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Inflammation Mediators
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Interleukin-17
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MIRN21 microRNA, mouse
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MicroRNAs
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Pdcd4 protein, mouse
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RNA-Binding Proteins
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Receptors, Transforming Growth Factor beta
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Interferon-gamma
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Protein Serine-Threonine Kinases
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Receptor, Transforming Growth Factor-beta Type II