Evaluation of the metal binding sites in a recombinant coagulation factor VIII identifies two sites with unique metal binding properties

Biol Chem. 2013 Jun;394(6):761-5. doi: 10.1515/hsz-2012-0298.

Abstract

Coagulation factor VIII is a glycosylated, non-covalent heterodimer consisting of a heavy chain (A1-A2-B domains) and a light chain (A3-C1-C2 domains). The association of the chains, and the stability and function of the dimer depend on the presence of metal ions. We applied X-ray fluorescence, X-ray crystallographic structure determination with anomalous signals at different wavelengths, and colorimetric measurements to evaluate the metal binding sites in a recombinant factor VIII molecule, turoctocog alfa. We identified a metal binding site in domain A3 dominated by Cu(+) binding and a site in domain A1 dominated by Zn(2+) binding.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Binding Sites
  • Calcium / chemistry
  • Calcium / metabolism
  • Colorimetry
  • Copper / chemistry
  • Copper / metabolism
  • Factor VIII / chemistry*
  • Factor VIII / metabolism*
  • Metals / chemistry
  • Metals / metabolism*
  • Models, Molecular
  • Protein Binding
  • Spectrometry, X-Ray Emission
  • Zinc / chemistry
  • Zinc / metabolism

Substances

  • Metals
  • recombinant factor VIII N8
  • Copper
  • Factor VIII
  • Zinc
  • Calcium