Diminished Th17 (not Th1) responses underlie multiple sclerosis disease abrogation after hematopoietic stem cell transplantation

Ann Neurol. 2013 Mar;73(3):341-54. doi: 10.1002/ana.23784. Epub 2013 Mar 5.

Abstract

Objective: To define changes in phenotype and functional responses of reconstituting T cells in patients with aggressive multiple sclerosis (MS) treated with ablative chemotherapy and autologous hematopoietic stem cell transplantation (HSCT).

Methods: Clinical and brain magnetic resonance imaging measures of disease activity were monitored serially in patients participating in the Canadian MS HSCT Study. Reconstitution kinetics of immune-cell subsets were determined by flow cytometry, whereas thymic function was assessed using T-cell receptor excision circle analyses as well as flow cytometry measurements of CD31+ recent thymic emigrants (RTEs). Functional assays were performed to track central nervous system-autoreactive antigen-specific T-cell responses, and the relative capacity to generate Th1, Th17, or Th1/17 T-cell responses.

Results: Complete abrogation of new clinical relapses and new focal inflammatory brain lesions throughout the 2 years of immune monitoring following treatment was associated with sustained decrease in naive T cells, in spite of restoration of both thymic function and release of RTEs during reconstitution. Re-emergence as well as in vivo expansion of autoreactive T cells to multiple myelin targets was evident in all patients studied. The reconstituted myelin-specific T cells exhibited the same Th1 and Th2 responses as preablation myelin-reactive T cells. In contrast, the post-therapy T-cell repertoire exhibited a significantly diminished capacity for Th17 responses.

Interpretation: Our results indicate that diminished Th17 and Th1/17 responses, rather than Th1 responses, are particularly relevant to the abrogation of new relapsing disease activity observed in this cohort of patients with aggressive MS following chemoablation and HSCT.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Antigens, CD / metabolism
  • Cell Movement / drug effects
  • Cell Proliferation / drug effects
  • Cytokines / metabolism
  • Female
  • Flow Cytometry
  • Follow-Up Studies
  • Glatiramer Acetate
  • Hematopoietic Stem Cell Transplantation / methods*
  • Humans
  • Immunosuppressive Agents / pharmacology
  • Immunosuppressive Agents / therapeutic use
  • Lymphocyte Activation / drug effects
  • Lymphocyte Activation / immunology*
  • Lymphocyte Count
  • Lymphokines / pharmacology
  • Male
  • Multiple Sclerosis / pathology*
  • Multiple Sclerosis / surgery*
  • Myelin Basic Protein / metabolism
  • Myelin-Oligodendrocyte Glycoprotein / metabolism
  • Peptides / pharmacology
  • Peptides / therapeutic use
  • Th1 Cells / drug effects
  • Th1 Cells / pathology
  • Th17 Cells / drug effects
  • Th17 Cells / immunology*
  • Th17 Cells / pathology*

Substances

  • Antigens, CD
  • Cytokines
  • Immunosuppressive Agents
  • Lymphokines
  • Myelin Basic Protein
  • Myelin-Oligodendrocyte Glycoprotein
  • Peptides
  • antigen-specific helper factors
  • Glatiramer Acetate