C1 inhibitor concentrate treatment of multiple laryngeal attacks in a 53-year-old woman with hereditary angioedema

Immunotherapy. 2013 Aug;5(8):855-7. doi: 10.2217/imt.13.53. Epub 2013 May 7.

Abstract

This report describes a woman who experienced a high number of laryngeal hereditary angioedema (HAE) attacks during her participation in the IMPACT2 clinical trial of C1-INH concentrate. A 53-year-old caucasian female with a 31-year history of type 1 HAE experienced 16 laryngeal HAE attacks between 3 August 2006 and 23 February 2010, 15 of which were severe. All laryngeal attacks were successfully treated with C1-INH 20 U/kg, with a median onset of relief of 14 min and median time to complete resolution of symptoms of 20 h, and no need for redosing. The reliable success of C1-INH for these potentially fatal events is reassuring for both patients and prescribers.

Publication types

  • Case Reports

MeSH terms

  • Complement C1 Inactivator Proteins / metabolism
  • Complement C1 Inhibitor Protein / administration & dosage*
  • Female
  • Hereditary Angioedema Types I and II / drug therapy*
  • Humans
  • Injections, Intravenous
  • Laryngeal Diseases / drug therapy*
  • Middle Aged
  • Pharmaceutical Preparations
  • Treatment Outcome

Substances

  • Complement C1 Inactivator Proteins
  • Complement C1 Inhibitor Protein
  • Pharmaceutical Preparations
  • SERPING1 protein, human